The following case is about a 15 year old male patient, who comes to a second level hospital for presenting abdominal distension and pain of eight months of evolution. Laboratory and imaging tests were performed, including: upper abdominal ultrasound, Doppler ultrasound and computed angiotomography of the abdomen, which led to the diagnosis of Budd Chiari Syndrome and proceeded to investigate the probable etiology of the condition, reporting elevated titers of anticardiolipin antibodies and lupus anticoagulant.