Exogenous lipid pneumonia is a rare nosological entity. It is an adult pathology whose frequency increases with age. The aim of this study is to examine the clinical and radiological presentation of lipid pneumonia, and to define the diagnostic and therapeutic strategies. Exposure to the causative agent is usually chronic. However, cases secondary to a single accidental exposure have been reported. The course of the disease is usually stable or slowly worsening, leading to impaired ventilatory function. Diagnosis of PLE is often delayed and difficult, due to a presentation that can be misleading in the absence of prior exposure. Treatment remains uncodified. However, avoidance of exposure at an early stage is an effective means of treatment, enabling lesions to regress or remain stable.