Giant cell tumor of the tendon sheath (GCTT) and pigmented vellonodular synovitis (PVNS) have often been considered as different nosological entities, the truth is that they represent a diverse group of proliferative lesions of the synovium that share identical histological features, both forms are different manifestations of the same disease.We propose our work as a way of didactic organization of this disease and its clinical forms, grouping varied and dispersed criteria available in the publications made by the scientific community, as a modest contribution in the training of the new generations of orthopedists; deepening in intrarticular SVNP and in the giant cell tumor of the tendon sheath.